Fig. 1 · Structure
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3-Hydroxyisovalerylcarnitine
MCD Diagnostic Marker
3-Hydroxyisovalerylcarnitine is a carnitine derivative that serves as a diagnostic marker for biotin deficiency. Elevated levels of this compound in plasma indicate reduced activity of biotin-dependent 3-methylcrotonyl-CoA carboxylase, disrupting the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA and impairing leucine catabolism. This makes 3-Hydroxyisovalerylcarnitine a useful biomarker for assessing biotin deficiency in research applications related to metabolic disorders.
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Specifications
| Manufacturer | Adooq Bioscience |
|---|---|
| CAS Number | 99159-87-2 |
| Applications | MCD Diagnostic Marker |
| Formula | C12H23NO5 |
| Molecular Weight | 261.31 |
| SMILES | CC(O)(CC(O[C@@H](C[N+](C)(C)C)CC([O-])=O)=O)C |
Storage & Solubility
In Vitro Solubility
Reported Solubility
No reported solubility data are available for this product.
Preparing Stock Solutions
| Concentration | |
|---|---|
Values use four significant digits. Prepare to the final solution volume; this is not the volume of solvent to add.
Stock preparation is unavailable for this product molecular weight.
Calculated stock concentrations do not establish solvent solubility. Refer to the reported solubility data for experimental guidance.
Storage
Store powder at -20°C, keep desiccated.
In powder form, the chemical is stable for 36 months.
In solution, store at -20°C and use within 1 month to prevent loss of potency. Aliquot to avoid multiple freeze/thaw cycles.